Usher syndrome is the most common condition that affects both hearing and vision. A syndrome is a disease or disorder that has more than one feature or symptom. The major symptoms of Usher syndrome are hearing loss and an eye disorder called retinitis pigmentosa, or RP. Retinitis pigmentosa causes night-blindness and a loss of peripheral vision (side vision) through the progressive degeneration of the retina. The retina is a light-sensitive tissue at the back of the eye and is crucial for vision. As retinitis pigmentosa progresses, the field of vision narrows, a condition known as “tunnel vision,” until only central vision (the ability to see straight ahead) remains. Many people with Usher syndrome also have severe balance problems.
Usher syndrome is inherited as an autosomal recessive trait that affects both hearing and vision. The major symptoms of Usher syndrome are hearing loss and an eye disorder called retinitis pigmentosa, or RP.
Usher Syndrome News
Eye Health Resources
- Eye Health Organizations Database
- Finding an Eye Care Professional
- Financial Aid for Eye Care
- Talking to Your Doctor
- Facts About Clinical Trials in Vision Research
- Videocasts on Vision Science and Eye Health, Archive
- Photo and Image Catalog
- Information in Spanish (Información en español)